Rhabdomyosarcoma (RMS) is a highly malignant neoplasm that arises from embryonic mesenchyme [1]. It is the most common soft tissue tumour in children, with the head and neck region accounting for 35-40% of cases [2]. Para meningeal (PM) rhabdomyosarcomas are tumors that arise from sites adjacent to the meninges, including the nasopharynx and nasal cavity, middle ear and mastoid, para nasal sinuses, pterygopalatine and infratemporal fossa. They have a propensity for central nervous system extension and poorer survival than the others rhabdomyosarcoma.
